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Sonia Franciosi

Specific Loss of Brain ABCA1 Increases Brain Cholesterol Uptake and Influences Neuronal Structure and Function
2009 · Joanna M. Karasinska, Franz Rinninger, et al. · Journal of Neuroscience · 150
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The role of the autonomic nervous system in arrhythmias and sudden cardiac death
2017 · Sonia Franciosi, Frances K.G. Perry, et al. · Autonomic Neuroscience · 143
Marked differences in neurochemistry and aggregates despite similar behavioural and neuropathological features of Huntington disease in the full-length BACHD and YAC128 mice
2012 · M. A. Pouladi, L. M. Stanek, et al. · Human Molecular Genetics · 138
Minocycline inhibits neuronal death and glial activation induced by β‐amyloid peptide in rat hippocampus
2004 · Jae K. Ryu, Sonia Franciosi, et al. · Glia · 129
Age-dependent neurovascular abnormalities and altered microglial morphology in the YAC128 mouse model of Huntington disease
2011 · Sonia Franciosi, Jae K. Ryu, et al. · Neurobiology of Disease · 128
HACE1 reduces oxidative stress and mutant Huntingtin toxicity by promoting the NRF2 response
2014 · Barak Rotblat, Amber L. Southwell, et al. · Proceedings of the National Academy of Sciences · 111
Anti-semaphorin 4D immunotherapy ameliorates neuropathology and some cognitive impairment in the YAC128 mouse model of Huntington disease
2015 · Amber L. Southwell, Sonia Franciosi, et al. · Neurobiology of Disease · 110
Altered palmitoylation and neuropathological deficits in mice lacking HIP14
2011 · R. R. Singaraja, K. Huang, et al. · Human Molecular Genetics · 108
ABCA1 influences neuroinflammation and neuronal death
2013 · Joanna M. Karasinska, Willeke de Haan, et al. · Neurobiology of Disease · 104
A fully humanized transgenic mouse model of Huntington disease
2012 · Amber L. Southwell, Simon C. Warby, et al. · Human Molecular Genetics · 102
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YB-1 Bridges Neural Stem Cells and Brain Tumor–Initiating Cells via Its Roles in Differentiation and Cell Growth
2011 · Abbas Fotovati, Samah Abu-Ali, et al. · Cancer Research · 91
IL-8 enhancement of amyloid-beta (Aβ1-42)-induced expression and production of pro-inflammatory cytokines and COX-2 in cultured human microglia
2004 · Sonia Franciosi, Hyun B. Choi, et al. · Journal of Neuroimmunology · 87
Preventing mutant huntingtin proteolysis and intermittent fasting promote autophagy in models of Huntington disease
2018 · Dagmar E. Ehrnhoefer, Dale D. O. Martin, et al. · Acta Neuropathologica Communications · 82
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Rescue from excitotoxicity and axonal degeneration accompanied by age-dependent behavioral and neuroanatomical alterations in caspase-6-deficient mice
2012 · Valeria Uribe, Bibiana K.Y. Wong, et al. · Human Molecular Genetics · 78
An International Multicenter Cohort Study on β-Blockers for the Treatment of Symptomatic Children With Catecholaminergic Polymorphic Ventricular Tachycardia
2021 · Puck J. Peltenburg, Dania Kallas, et al. · Circulation · 73
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Natural history of disease in the YAC128 mouse reveals a discrete signature of pathology in Huntington disease
2011 · Jeffrey B. Carroll, Jason P. Lerch, et al. · Neurobiology of Disease · 73
Extensive proteomic screening identifies the obesity-related NYGGF4 protein as a novel LRP1-interactor, showing reduced expression in early Alzheimer's disease
2010 · Yuji Kajiwara, Sonia Franciosi, et al. · Molecular Neurodegeneration · 72
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Hip14l-deficient mice develop neuropathological and behavioural features of Huntington disease
2012 · Liza M. Sutton, Shaun S. Sanders, et al. · Human Molecular Genetics · 70
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Broad-Spectrum Effects of 4-Aminopyridine to Modulate Amyloid β1–42-Induced Cell Signaling and Functional Responses in Human Microglia
2006 · Sonia Franciosi, Jae K. Ryu, et al. · Journal of Neuroscience · 68
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Laquinimod rescues striatal, cortical and white matter pathology and results in modest behavioural improvements in the YAC128 model of Huntington disease
2016 · Marta Garcia-Miralles, Xin Hong, et al. · Scientific Reports · 66
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Clinical and Functional Characterization of Ryanodine Receptor 2 Variants Implicated in Calcium-Release Deficiency Syndrome
2021 · Thomas M. Roston, Jinhong Wei, et al. · JAMA Cardiology · 61
Burst Exercise Testing Can Unmask Arrhythmias in Patients With Incompletely Penetrant Catecholaminergic Polymorphic Ventricular Tachycardia
2021 · Thomas M. Roston, Dania Kallas, et al. · JACC. Clinical electrophysiology · 59
A Huntingtin-based peptide inhibitor of caspase-6 provides protection from mutant Huntingtin-induced motor and behavioral deficits
2015 · Israel Aharony, Dagmar E. Ehrnhoefer, et al. · Human Molecular Genetics · 59
Memory and synaptic deficits in Hip14/DHHC17 knockout mice
2013 · Austen J. Milnerwood, Matthew P. Parsons, et al. · Proceedings of the National Academy of Sciences · 52
Pepsin pretreatment allows collagen IV immunostaining of blood vessels in adult mouse brain
2007 · Sonia Franciosi, Rita De Gasperi, et al. · Journal of Neuroscience Methods · 52
Works count: 157
Citation count: 3,085
H-index: 33
I10-index: 53
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