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Author

Sofía García

Observed names: S Garcia, Sofia Garcia
Institution: University of Miami
ORCID: 0000-0003-3809-1510
Observed ORCID: 0000-0003-3809-1510
OpenAlex ID: A5101736386
Cytochrome c Oxidase Is Required for the Assembly/Stability of Respiratory Complex I in Mouse Fibroblasts
2006 · Francisca Diaz, Hirokazu Fukui, et al. · Molecular and Cellular Biology · 236
Mice lacking COX10 in skeletal muscle recapitulate the phenotype of progressive mitochondrial myopathies associated with cytochrome c oxidase deficiency
2005 · Francisca Diaz, Christine K. Thomas, et al. · Human Molecular Genetics · 179
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A defect in the mitochondrial complex III, but not complex IV, triggers early ROS-dependent damage in defined brain regions
2012 · Francisca Diaz, Sofia Garcia, et al. · Human Molecular Genetics · 110
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ATAD3 controls mitochondrial cristae structure in mouse muscle, influencing mtDNA replication and cholesterol levels
2018 · Susana Peralta, Steffi Goffart, et al. · Journal of Cell Science · 109
Organ-specific shifts in mtDNA heteroplasmy following systemic delivery of a mitochondria-targeted restriction endonuclease
2010 · S R Bacman, S L Williams, et al. · Gene Therapy · 106
ATAD3A has a scaffolding role regulating mitochondria inner membrane structure and protein assembly
2021 · Tania Arguello, Susana Peralta, et al. · Cell Reports · 88
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Overexpression of PGC ‐1α in aging muscle enhances a subset of young‐like molecular patterns
2018 · Sofia Garcia, Nadee Nissanka, et al. · Aging Cell · 82
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Pathophysiology and fate of hepatocytes in a mouse model of mitochondrial hepatopathies
2007 · F Diaz, S Garcia, et al. · Gut · 52
Long-Term Bezafibrate Treatment Improves Skin and Spleen Phenotypes of the mtDNA Mutator Mouse
2012 · Lloye M. Dillon, Aline Hida, et al. · PLoS ONE · 44
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Partial complex I deficiency due to the CNS conditional ablation of Ndufa5 results in a mild chronic encephalopathy but no increase in oxidative damage
2013 · Susana Peralta, Alessandra Torraco, et al. · Human Molecular Genetics · 42
Sustained AMPK activation improves muscle function in a mitochondrial myopathy mouse model by promoting muscle fiber regeneration
2016 · Susana Peralta, Sofia Garcia, et al. · Human Molecular Genetics · 35
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The Organization of Mitochondrial Supercomplexes is Modulated by Oxidative Stress In Vivo in Mouse Models of Mitochondrial Encephalopathy
2018 · Mir R. Anwar, Amy Saldana-Caboverde, et al. · International Journal of Molecular Sciences · 23
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Metformin delays neurological symptom onset in a mouse model of neuronal complex I deficiency
2020 · Susana Peralta, Milena Pinto, et al. · JCI Insight · 21
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Enhanced glycolysis and GSK3 inactivation promote brain metabolic adaptations following neuronal mitochondrial stress
2021 · Sofia Garcia, Amy Saldana-Caboverde, et al. · Human Molecular Genetics · 17
Hypoxia Promotes Mitochondrial Complex I Abundance via HIF-1α in Complex III and Complex IV Deficient Cells
2020 · Amy Saldana-Caboverde, Nadee Nissanka, et al. · Cells · 14
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A 3′ UTR Modification of the Mitochondrial Rieske Iron Sulfur Protein in Mice Produces a Specific Skin Pigmentation Phenotype
2008 · Sofia Garcia, Francisca Diaz, et al. · Journal of Investigative Dermatology · 8
Metabolic adaptations in neurons with complex IV deficiency
2012 · Francisca Diaz, Sofia Garcia, et al. · Mitochondrion · 2
Regenerate to survive: Cytochrome oxidase deficiency in hepatocytes
2006 · Francisca Diaz, Sofia Garcia, et al. · Mitochondrion · 1
Organ-specific shifts in mtDNA heteroplasmy following systemic delivery of a mitochondria-targeted restriction endonuclease
2011 · Sandra R. Bacman⁎, Sion L. Williams, et al. · Mitochondrion
32 Systemic delivery of mitochondria-targeted restriction endonucleases to alter mtDNA heteroplasmy in specific tissue
2010 · Sandra R. Bacman, Sion L. Williams, et al. · Mitochondrion
65 Phenotypic differences of animal models of complex III and complex IV deficiencies in neurons
2010 · Francisca Diaz, Sofia Garcia, et al. · Mitochondrion
Works count: 22
Citation count: 1,169
H-index: 14
I10-index: 15
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