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Hans R. Scholte

Observed names: H R Scholte, H SCHOLTE, H. R. SCHOLTE, H. R. Scholte, H. R. Scholte A, H. Scholte, H. Steven Scholte, H.R. SCHOLTE, H.R. Scholte, HANS R. SCHOLTE, HR Scholte, Hans R Scholte, Hans R Scholte Open Access, Hans Scholte, Scholte, H. R., Scholte, H.R., Scholte, Hans R.
Institution: Erasmus MC
Observed institutions: Leiden University, University Medical Center Groningen, Inserm, University of Groningen, Utrecht University, Erasmus MC, Amsterdam UMC Location University of Amsterdam, Maastricht University, Emma Kinderziekenhuis, Erasmus MC - Sophia Children’s Hospital, Academisch Ziekenhuis Rotterdam, Syracuse University, Vrije Universiteit Amsterdam, University of Amsterdam, Erasmus University Rotterdam, McMaster University
OpenAlex ID: A5111533688
An X-linked mitochondrial disease affecting cardiac muscle, skeletal muscle and neutrophil leucocytes
1983 · P.G. Barth, H.R. Scholte, et al. · Journal of the Neurological Sciences · 704
NADH-CoQ REDUCTASE DEFICIENT MYOPATHY: SUCCESSFUL TREATMENT WITH RIBOFLAVIN
1983 · W.F.M. Arts, H.R. Scholte, et al. · The Lancet · 438
Clear Correlation of Genotype with Disease Phenotype in Very–Long-Chain Acyl-CoA Dehydrogenase Deficiency
1999 · Brage Storstein Andresen, Simon Olpin, et al. · The American Journal of Human Genetics · 305
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Fatty Acid Activation: Specificity, Localization, and Function
1976 · P.H.E. GROOT, H.R. SCHOLTE, et al. · Advances in lipid research · 215
Genetic and biochemical impairment of mitochondrial complex I activity in a family with Leber hereditary optic neuropathy and hereditary spastic dystonia.
1996 · D D De Vries, L N Went, et al. · PubMed · 189
Patients with chronic fatigue syndrome performed worse than controls in a controlled repeated exercise study despite a normal oxidative phosphorylation capacity
2010 · Ruud CW Vermeulen, Ruud M Kurk, et al. · Journal of Translational Medicine · 142
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Riboflavin-responsive oxidative phosphorylation complex I deficiency caused by defective ACAD9: new function for an old gene
2010 · Mike Gerards, Bianca J. C. van den Bosch, et al. · Brain · 132
A rapid and simple procedure to deplete rat-liver mitochondria of lysosomal activity
1970 · J. Loewenstein, H.R. Scholte, et al. · Biochimica et Biophysica Acta (BBA) - Bioenergetics · 128
The localization of mitochondrial creatine kinase, and its use for the determination of the sidedness of submitochondrial particles
1973 · H.R. Scholte, P.J. Weijers, et al. · Biochimica et Biophysica Acta (BBA) - Biomembranes · 118
On the triple localization of creatine kinase in heart and skeletal muscle cells of the rat: Evidence for the existence of myofibrillar and mitochondrial isoenzymes
1973 · H.R. Scholte · Biochimica et Biophysica Acta (BBA) - Bioenergetics · 106
X‐linked cardioskeletal myopathy and neutropenia (Barth syndrome): Respiratory‐chain abnormalities in cultured fibroblasts
1996 · P. G. Barth, C. Van den Bogert, et al. · Journal of Inherited Metabolic Disease · 99
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The biochemical basis of mitochondrial diseases
1988 · H. R. Scholte · Journal of Bioenergetics and Biomembranes · 97
Exome sequencing reveals a novel Moroccan founder mutation inSLC19A3as a new cause of early-childhood fatal Leigh syndrome
2013 · Mike Gerards, Rick Kamps, et al. · Brain · 95
Riboflavin-responsive complex I deficiency
1995 · H.R. Scholte, H.F.M. Busch, et al. · Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease · 83
A Fatal, Systemic Mitochondrial Disease with Decreased Mitochondrial Enzyme Activities, Abnormal Ultrastructure of the Mitochondria and Deficiency of Heat Shock Protein 60
1993 · E. Agsteribbe, A. Huckriede, et al. · Biochemical and Biophysical Research Communications · 83
Depletion of mitochondrial deoxyribonucleic acid in a family with fatal neonatal liver disease
1996 · Henk D. Bakker, Hans R. Scholte, et al. · The Journal of Pediatrics · 82
Carnitine palmitoyltransferase II deficiency with normal carnitine palmitoyltransferase I in skeletal muscle and leucocytes
1979 · H.R. Scholte, F.G.I. Jennekens, et al. · Journal of the Neurological Sciences · 82
The intracellular and intramitochondrial distribution of malonyl-CoA decarboxylase and propionyl-CoA carboxylase in rat liver
1969 · H.R. Scholte · Biochimica et Biophysica Acta (BBA) - Enzymology · 82
Primary carnitine deficiency.
1990 · H R Scholte, R Rodrigues Pereira, et al. · PubMed · 81
Mitochondrial Injury Lessons from the Fialuridine Trial
1997 · Pieter Honkoop, Hans R. Scholte, et al. · Drug Safety · 78
Defective complex I assembly due to C20orf7 mutations as a new cause of Leigh syndrome
2009 · M Gerards, W Sluiter, et al. · Journal of Medical Genetics · 70
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Exploratory Open Label, Randomized Study of Acetyl- and Propionylcarnitine in Chronic Fatigue Syndrome
2004 · Ruud C. W. Vermeulen, Hans R. Scholte · Psychosomatic Medicine · 70
Efficacy of carnitine in the treatment of children with attention-deficit hyperactivity disorder
2002 · L.J. Van Oudheusden, H.R. Scholte · Prostaglandins Leukotrienes and Essential Fatty Acids · 70
Identification of two novel mutations in OCTN2 of three patients with systemic carnitine deficiency
1999 · F.M. Vaz, H.R. Scholte, et al. · Human Genetics · 69
Carnitine palmitoyltransferase deficiencies
1985 · HANS R. SCHOLTE, WILLEM C. HÜLSMANN, et al. · Biochemical Society Transactions · 68
Works count: 165
Citation count: 6,038
H-index: 42
I10-index: 100
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