Haissaguerre syndrome--a new clinical entity in the spectrum of primary electrical diseases?
Year: 2009
Type: article
Abstract: Sudden cardiac death (SCD) is an important issue worldwide and occurs at a rate of 0.36 to 1.28 per 1000 persons/year in the US [1]. Approximately 10% of SCD cases occur in patients with no evidence of structural heart disease. Channelopathies are primary electrical diseases that are responsible for the majority these SCD cases. At the end of the 20th century, two new arrhythmic syndromes were identified as channelopathies – Brugada syndrome (BrS) (1992) and short QT syndrome (2000) – and these have received considerable interest in recent years [2, 3]. Although specific electrocardiographic hallmarks are present in channelopathies, often these ECG signs can be transient and difficult to detect. A SCD caused by ventricular fibrillation (VF) in a patient without a specific ECG sign is described as an idiopathic VF (IVF). Recently, some IVF episodes or SCDs have been reported to be associated with the presence of prominent J-waves or J-point elevation in inferior and/or lateral leads [4-15].
Source: PubMed
Authors: Piotr Kukla, Marek Jastrzebski
Language: English
Subfield: Cardiology and Cardiovascular Medicine
Field: Medicine
Domain: Health Sciences
Open Access status: green
OpenAlex ID: W158850824