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Perichondrium phenotype and border function are regulated by Ext1 and heparan sulfate in developing long bones: A mechanism likely deranged in Hereditary Multiple Exostoses

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Year: 2013
Type: article
Source: Developmental Biology
DOI: 10.1016/j.ydbio.2013.02.008
Authors: Julianne Huegel, Christina Mundy, Federica Sgariglia, Patrik Nygren, Paul C. Billings, Yu Yamaguchi, Eiki Koyama, Maurizio Pacifici
Institutions: Children's Hospital of Philadelphia, Temple University, University of Pennsylvania, Sanford Burnham Prebys Medical Discovery Institute
Language: English

Topic: Bone Tumor Diagnosis and Treatments
Subfield: Rheumatology
Field: Medicine
Domain: Health Sciences
SDG: Good health and well-being

Open Access status: bronze

Funders: National Institutes of Health, National Institute of Arthritis and Musculoskeletal and Skin Diseases, National Institute of Dental and Craniofacial Research
Awards: G1048271666, Heparan Sulfate in Skeletal Development and Diseases, Hereditary Multiple Exostosis Syndrome: Pathogenesis and Treatment, Pathogenic Mechanisms in Hereditary Multiple Exostoses Syndrome
OpenAlex ID: W1990242254
FWCI: 6.259
Cites: 69
Cited by: 65
Related to: 10
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