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The optimized allotopic expression of ND1 or ND4 genes restores respiratory chain complex I activity in fibroblasts harboring mutations in these genes

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Year: 2008
Type: article
Source: Biochimica et Biophysica Acta (BBA) - Molecular Cell Research
DOI: 10.1016/j.bbamcr.2008.04.018
Authors: Crystel Bonnet, Sébastien Augustin, Sami Ellouze, Paule Bénit, Aicha Bouaita, Pierre Rustin, José-Alain Sahel, Marisol Corral-Debrinski
Institutions: Institut de la Vision, Inserm, Université Pierre-et-Marie-Curie, Hôpital Robert-Debré, NeuroDiderot, Centre hospitalier national d'ophtalmologie des Quinze-Vingts
Language: English

Topic: Mitochondrial Function and Pathology
Subfield: Molecular Biology
Field: Biochemistry, Genetics and Molecular Biology
Domain: Life Sciences
SDG: Good health and well-being

Open Access status: bronze

Funders: Agence Nationale de la Recherche, Institut National de la Santé et de la Recherche Médicale, Institut Carnot Santé Animale, Retina France
OpenAlex ID: W2053558205
FWCI: 2.591
Cites: 49
Cited by: 129
Related to: 10
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