Work

Cruveilhier-Baumgarten disease in a patient with turner syndrome: Case report of a rare indication for liver transplantation

Year: 2008

Type: article

Abstract: Some chromosomal alterations can be associated with vascular abnormalities. For instance, Turner syndrome can be complicated by agenesis or hypoplasia of the portal venous system causing presinusoidal portal hypertension. Liver transplantation to treat this condition overcomes portal hypertension and reconstitutes the diminished hepatic function due to severe atrophy of the portal venous inflow.

Source: Liver Transplantation

DOI: 10.1002/lt.21374

Authors: Federico Aucejo, Zuhaib Ibrahim, Koji Hashimoto, Cristiano Quintini, Dympna Kelly, David Vogt, Bijan Eghtesad, John Fung, Charles Miller, Ralph Tuthill

Institution: Cleveland Clinic

Language: English

Topic: Liver Disease and Transplantation

Subfield: Hepatology

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: bronze

OpenAlex ID: W2094472832

FWCI: 0.212

Cites: 14

Cited by: 6

Related to: 10