Clinical evaluation, medical management and outcome of atrioventricular canal defects
Year: 1999
Type: article
Abstract: The relative effects of interatrial shunting, interventricular shunting and atrioventricular valve function will determine the general course of patients with atrioventricular canal defects. This report reviews the natural history, medical management and current outcome of this group of patients. The overall long-term survival of patients with primum atrial septal defect following repair was found to match that of the general population. Results following complete AV canal repair have similarly improved significantly in the last decade. However, residual mitral valve dysfunction remains an important post-operative issue. Straddling, stenosis or atresia of part of the AV valve, often results in significant hypoplasia of a ventricular chamber. In extreme cases, the management will generally follow that of other single ventricle variants, eventually resulting in Fontan palliation. The clinical course and outcome of these and other complex variants such as atrioventricular canal defect with tetralogy of Fallot is discussed.
Source: Progress in Pediatric Cardiology
Authors: Howard D. Apfel, Welton M. Gersony
Language: English
Subfield: Epidemiology
Field: Medicine
Domain: Health Sciences
Open Access status: hybrid
Estimated APC paid: $2,670
OpenAlex ID: W2163206762