Work

Case report: Giant congenital pulmonary airway malformation initially managed and resected on ECMO

Year: 2016

Type: article

Abstract: Congenital pulmonary airway malformations (CPAM) are a common congenital anomaly, occurring as a result of aberrant formation of pulmonary lobes or segments. Many patients with CPAM are treated with postnatal surgical excision within 1-year of age. CPAM that are enlarged to the point of causing an intrathoracic mass effect may cause hydrops fetalis. Fetuses affected in this way may require prenatal intervention and immediate postnatal intervention. We herein report a case of a large CPAM causing hydrops fetalis and postnatal respiratory failure, treated by an aggressive prenatal and postnatal multidisciplinary approach, culminating in resection of the lesion while on extracorporeal membrane oxygenation (ECMO) support.

Source: Journal of Pediatric Surgery Case Reports

DOI: 10.1016/j.epsc.2016.04.003

Authors: Richard Yeker, Bradley Segura, Daniel Saltzman, Donavon Hess

Institution: University of Minnesota

Language: English

Topic: Congenital Diaphragmatic Hernia Studies

Subfield: Surgery

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: gold

Estimated APC paid: $1,130