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Lung function decline is delayed but not decreased in patients with cystic fibrosis and the R117H gene mutation

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Year: 2017
Type: article
Study design: Observational Study
Source: Journal of Cystic Fibrosis
DOI: 10.1016/j.jcf.2017.10.003
Authors: Jeffrey S. Wagener, Stefanie J. Millar, Nicole Mayer-Hamblett, Gregory S. Sawicki, Edward F. McKone, Christopher H. Goss, Michael W. Konstan, Wayne J. Morgan, David J. Pasta, Richard B. Moss
Institutions: University of Colorado Anschutz, University of Colorado Denver, University of Washington, Cystic Fibrosis Foundation, Harvard University, St. Vincent's University Hospital, Case Western Reserve University, University of Arizona, Stanford University
Language: English

Topic: Cystic Fibrosis Research Advances
Subfield: Pulmonary and Respiratory Medicine
Field: Medicine
Domain: Health Sciences
SDG: Good health and well-being

Open Access status: bronze

Funders: Cystic Fibrosis Foundation, Vertex Pharmaceuticals, National Institute of Diabetes and Digestive and Kidney Diseases
Award: Center for Cystic Fibrosis Translational Research in the Post-CFTR modulator Era
OpenAlex ID: W2765579927
FWCI: 2.715
Cites: 19
Cited by: 18
Related to: 10
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