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Ivacaftor-treated Patients with Cystic Fibrosis Derive Long-Term Benefit Despite No Short-Term Clinical Improvement

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Year: 2017
Type: article
Source: American Journal of Respiratory and Critical Care Medicine
DOI: 10.1164/rccm.201710-2046le
Authors: Sonya L. Heltshe, Steven M. Rowe, Michelle Skalland, Arthur Baines, Manu Jain
Institutions: University of Washington, Cystic Fibrosis Foundation, University of Alabama, University of Alabama at Birmingham, Northwestern University
Language: English

Topic: Cystic Fibrosis Research Advances
Subfield: Pulmonary and Respiratory Medicine
Field: Medicine
Domain: Health Sciences
SDG: Good health and well-being

Open Access status: green

Funders: Cystic Fibrosis Foundation, Cystic Fibrosis Foundation Therapeutics, Northwestern University, University of Washington, National Institutes of Health, Feinberg School of Medicine, National Heart, Lung, and Blood Institute, National Institute of Diabetes and Digestive and Kidney Diseases, National Center for Advancing Translational Sciences
Awards: Translational Program in CFTR-Related Airway Diseases, G308544354, G3913178333, G691201058, G694332062, Center for Cystic Fibrosis Translational Research in the Post-CFTR modulator Era
OpenAlex ID: W2806303552
FWCI: 2.028
Cites: 12
Cited by: 27
Related to: 10
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