Work

The pulseless patient: Profound vasculopathy as the presenting feature of fulminant dermatomyositis and response to therapy

Year: 2019

Type: article

Abstract: The idiopathic inflammatory myopathies are uncommon childhood conditions that present with proximal muscle weakness and characteristic cutaneous manifestations. Juvenile dermatomyositis (JDM) is the most common subtype, comprising 80% to 85% of cases.1 The overall prognosis of JDM has improved considerably over the last few decades because of more aggressive use of corticosteroids and other immunosuppressant medications.2 JDM is known to cause myriad symptoms that can vary from patient to patient, including calcinosis cutis, ulcerations, and, most significantly, cutaneous and systemic vasculopathy.

Source: JAAD Case Reports

DOI: 10.1016/j.jdcr.2018.11.011

Authors: Farzam Gorouhi, Maija Kiuru, Marc Silverstein, Parisa Emami-Naeini, Susanna S. Park, Danielle Tartar

Institution: University of California, Davis

Language: English

Topic: Inflammatory Myopathies and Dermatomyositis

Subfield: Epidemiology

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: gold

Estimated APC paid: $600