Angio-Behçet: When Arterial Atypia Is at The Heart of The Disease: About Three Observations
Year: 2024
Type: article
Study design: Case Report
Abstract: Behçet's disease is a systemic vasculitis, the etiology of which remains obscure. Ocular, cutaneous, articular, neurological, and vascular involvement remain the most significant. We report a series of 3 cases of Behçet's disease with atypical arterial vascular manifestations, collected in an internal medicine department. The majority of our patients, with an average age of 45 years at the onset of arterial involvement, were male, with only one female. The arterial manifestations observed were mainly characterized by atypical locations, including visceral arteries, and presented as arterial occlusions. Corticosteroid therapy was necessary in all cases, in combination with other treatments such as anticoagulants, colchicine, and immunosuppressants. Overall, the outcome was favorable for the majority of patients. In the literature, arterial involvement is much less frequent than venous involvement, mainly affecting the aorta and pulmonary arteries, and manifesting primarily as aneurysms or pseudoaneurysms, even less frequently as occlusions, and notably with rare or even exceptional locations found in very few studies, making our observations original. However, arterial involvement poses therapeutic challenges due to its recurrent nature, which can impact prognosis.
Authors: Bellamine H, Moudatir M, Echchilali K, Barakat L, Benzakour M, Elkabli H
Language: English
Subfield: Ophthalmology
Field: Medicine
Domain: Health Sciences
Open Access status: bronze
OpenAlex ID: W4400341780