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Ketone bodies resume mitochondrial respiration in neuronal progenitors from iPSCs of patients with AGC1 deficiency

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Year: 2024
Type: article
Source: Biochimica et Biophysica Acta (BBA) - Bioenergetics
DOI: 10.1016/j.bbabio.2024.149394
Authors: Francesco M. Lasorsa, Simona N. Barile, Maria C. Magnifico, Felix Distelmaier, Eleonora Poeta, Luigi Viggiano, Antonella Pignataro, Marica Antonicelli, Luigi Palmieri, Sabrina Petralla, Julia Hentschel, Vito Porcelli, Gaia Tioli, Isabella Pisano, Anna Maria Porcelli, Giuseppe Fiermonte, Ferdinando Palmieri, Stewart A. Anderson, Luisa Iommarini, Douglas C. Wallace, Barbara Monti
Institutions: Institute of Biomembranes, Bioenergetics and Molecular Biotechnologies, University of Bari Aldo Moro, Heinrich Heine University Düsseldorf, University of Bologna, University Hospital Leipzig, Children's Hospital of Philadelphia, University of Pennsylvania
Language: English

Topic: Mitochondrial Function and Pathology
Subfield: Molecular Biology
Field: Biochemistry, Genetics and Molecular Biology
Domain: Life Sciences
SDG: Good health and well-being

Open Access status: bronze
OpenAlex ID: W4401888175
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Related to: 10
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