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Congenital Nasal Pyriform Aperture Stenosis as a Rare Cause of Cyclical Cyanosis

Year: 2024

Type: article

Abstract: Congenital nasal pyriform aperture stenosis (CNPAS) is a rare condition affecting the upper airway system. Unlike choanal atresia, the symptom if any, can be insignificant or appear delayed. We report a case of a 3-month-old baby girl who had history of sudden brief episodes of cyanosis and desaturation during sleep and relieved upon awakening and crying. It was associated with intermittent stertor and required oxygen supplementation. The airway symptom worsened with rhinorrhea and nasal blockage, which required re-admission. The inability to introduce a suction catheter size 6 French and pediatric flexible scope size 2.2mm into bilateral nostrils was diagnostic.

Source: Malaysian Journal of Paediatrics and Child Health

DOI: 10.51407/mjpch.v30i2.294

Authors: Wan Nur Amirah Syahirah Wan Ali, Nor Shahida Abdul Mutalib, Azliana Aziz, Hazama Mohamad, Irfan Mohamad

Institutions: Universiti Sains Malaysia, Sultan Abdul Halim Hospital, Hospital Universiti Sains Malaysia

Language: English

Topic: Congenital Ear and Nasal Anomalies

Subfield: Genetics

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: diamond

OpenAlex ID: W4401924896

FWCI:

Cites: 4

Cited by:

Related to: 10