Year: 2024
Type: article
Study design: Case Report
Abstract: Background. Biliary atresia is the leading cause of liver transplantation in children. It is associated with other congenital anomalies. The presentation of biliary atresia with situs inversus is a rare case. Case presentation. A 2-month-old female presented with jaundice since 15 days of life, acolic stools, and tea-colored urine. On further evaluation, she was found to have dextrocardia and situs inversus. A liver biopsy was performed and showed hepatic fibrosis due to extrahepatic cholestasis. Abdominal ultrasound and MRCP confirmed a liver in the left hypochondrium and suggested biliary atresia. Conclusion. Although rare, every patient with biliary atresia should be screened for congenital situs inversus, which has a poor prognosis.
Source: Romanian Journal of Pediatrics
Institution: Universitas Airlangga
Language: English
Subfield: Surgery
Field: Medicine
Domain: Health Sciences
Open Access status: gold
Estimated APC paid: $216
OpenAlex ID: W4402923523