Work

A case of primary cutaneous marginal zone lymphoma in a 12‐year‐old with mast cell activating syndrome

Year: 2024

Type: editorial

Abstract: Primary cutaneous marginal zone lymphoma (PCMZL) is reported to primarily affect non-Hispanic Caucasian males over 50 years old. We present a case of a 16-year-old female with mast cell activation syndrome (MCAS) who developed PCMZL of the skin of both cheeks, left forearm and right arm. The patient was treated initially with intralesional steroids which successfully shrunk lesions on her face and left forearm. Rituximab and doxycycline were attempted but stopped due to severe allergic reactions and anaphylaxis. Ultimately, the remaining nodules on her right arm were surgically excised.

Source: Pediatric Blood & Cancer

DOI: 10.1002/pbc.31381

Authors: Madison Wnuk, Marjorie Montanez‐Wiscovich, Sthorn Thatayatikom, William B. Slayton

Institutions: UF Health Shands Hospital, University of Florida Health, University of Florida, UF Health Cancer Center, AdventHealth for Children

Language: English

Topic: Cutaneous lymphoproliferative disorders research

Subfield: Dermatology

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: green

OpenAlex ID: W4403353352

Cites: 7

Cited by: 1

Related to: 10