Work

Angiomatoid fibrous histiocytoma Ó? an adolescent with an unusual presentation and course

Year: 2024

Type: article

Abstract: Introduction: Angiomatoid fibrous histiocytoma is a rare soft tissue neoplasm, which usually presents as an indolent mass in children and young adults and is often mistaken for a hematoma or hemangioma. Suspecting this diagnosis from imaging findings may be challenging, leading to diagnostic delays. Prognosis is generally favorable and metastases are infrequent at presentation. Case report: We describe the case of an adolescent who presented with a two-month history of a growing mass in the left scapular region, where diagnosis was made possible through surgical biopsy. Discussion: There were loco-regional lymphatic invasions and lung metastases at admission, and despite surgery and chemotherapy the disease rapidly progressed to death.

Source: Portuguese Journal of Pediatrics

DOI: 10.24875/pjp.m24000458

Authors: Ana Lacerda, Cristina Mendes, Rafael Cabrera, Sara Isabel de Almeida, Sofia Cochito Sousa

Institutions: Instituto Português de Oncologia Francisco Gentil, Hospital Beatriz Ângelo, Centro Hospitalar Lisboa Norte, Hospital de Santa Maria

Language: English

Topic: Sarcoma Diagnosis and Treatment

Subfield: Pulmonary and Respiratory Medicine

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: diamond

OpenAlex ID: W4404130282