Work

Intra–Abdominal Desmoplastic Small Round Cell Tumor: A Rare Case Report and Review of Literature

Year: 2024

Type: article

Abstract: Desmoplastic small round cell tumor (DSRCT) is a rare and aggressive type of sarcomatous tumor with a high proclivity ofmetastasis.While it predominantly affects the abdominal cavity, it is most often observed in younger males and histopathologically identified by vascular and collagenous stroma containing groups of small tumor cells. However, standardized treatment approaches are currently unavailable. Here, we present the case of a 47-year-old man diagnosed with intra-abdominal metastatic DSRCT managed with multiple lines of chemotherapy followed by surgical debulking. Overall survival of 32 months is achieved with good quality of life.

Source: Indian Journal of Medical and Paediatric Oncology

DOI: 10.1055/s-0044-1790582

Authors: Ankur Mudgal, Devender Sharma, Vikram Singhal, Ashok Vaid

Institutions: Medanta The Medicity, Medanta The Medicity

Language: English

Topic: Sarcoma Diagnosis and Treatment

Subfield: Pulmonary and Respiratory Medicine

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: diamond

OpenAlex ID: W4405357699