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Bentall Procedure in a Marfan Syndrome Patient With Reduced Ejection Fraction: A Case Report

Year: 2024

Type: article

Abstract: Marfan syndrome (MFS) is an autosomal dominant disorder affecting the connective tissue, often leading to aortic root dilation, aneurysm, and dissection. We report on a 35-year-old Bangladeshi female patient with MFS who presented with chest pain, shortness of breath, and a significant aortic root aneurysm, along with a reduced ejection fraction (EF) of 20%-25%. Imaging confirmed significant aortic dilation, and due to the high risk of mortality, an urgent Bentall procedure was performed. Postoperatively, the patient had an EF of 25% and was doing well at discharge. Timely Bentall procedure in MFS with severe aortic root dilation and reduced EF is critical for improving outcomes and reducing morbidity and mortality.

Source: Cureus

DOI: 10.7759/cureus.76238

Authors: Ghadeer F Bu Saeed, Manal F Alshammari, Dana S Abalkhail, Yasser A Elghoneimy

Institution: Imam Abdulrahman Bin Faisal University

Language: English

Topic: Aortic Disease and Treatment Approaches

Subfield: Pulmonary and Respiratory Medicine

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: diamond

OpenAlex ID: W4405697336