Work

An unusual presentation of primary synovial sarcoma of the ethmoid sinus in a 54-year-old woman: A case report and literature review

Year: 2024

Type: article

Abstract: INTRODUCTION AND IMPORTANCE: Synovial sarcoma is a malignant soft tissue tumor primarily affects the extremities. Its presence in the paranasal sinuses, especially within the ethmoid sinus, is exceedingly rare. CASE PRESENTATION: We report a case of monophasic synovial sarcoma of the ethmoid sinus in a 54-year-old woman, who presented with 3 months history of left eye pain and bulging. CT with contrast, MRI, and histopathology confirmed the diagnosis. Whose management was partial surgical resection with postoperative chemotherapy and radiotherapy. Post-treatment, the patient showed a good clinical outcome and remained under regular follow-up care by the oncology team. CASE DISCUSSION: To our knowledge, there are only six reported cases of primary synovial sarcoma in the ethmoid sinus. Its atypical presentation and unspecific features make diagnosis challenging. Partial surgical resection with postoperative chemotherapy and radiotherapy is the standard treatment. However, the prognosis remains poor, with a high risk of recurrence, necessitating thorough follow-up. CONCLUSION: This case highlights the presentation and management of a significantly rare tumor in unusual body region.

Source: International Journal of Surgery Case Reports

DOI: 10.1016/j.ijscr.2024.110784

Authors: Hamza A. Abdul-Hafez, Reem A. Abu-Alrub, Mohammed A. Barakat, Ahmad Ziad Meri, Hanood Abu Rass

Institution: An-Najah National University

Language: English

Topic: Sarcoma Diagnosis and Treatment

Subfield: Pulmonary and Respiratory Medicine

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: gold

Estimated APC paid: $1,800