Posterior scleritis in an 18-year-old female with primary familial brain calcification syndrome: Incidental finding or association?
Year: 2025
Type: article
Study design: Case Report
Abstract: Primary familial brain calcification (PFBC) is an idiopathic neurological disease associated with intracranial calcification. An 18-year-old female, a known case of uncontrolled Type 1 diabetes mellitus, presented with unilateral progressive diminution of vision in her left eye. Based on her clinical examination, a diagnosis of left eye posterior scleritis was made. Computed tomography of the brain revealed bilateral caudate and lentiform nuclei patchy calcifications suggestive of Fahr's syndrome or PFBC. In our patient, age and posterior scleritis were two uncommon presentations to be associated with PFBC.
Source: Saudi Journal of Ophthalmology
Authors: Hala A. Khalil, Khaled Helaiwa
Institution: King Hamad University Hospital
Language: English
Subfield: Neurology
Field: Neuroscience
Domain: Life Sciences
Open Access status: hybrid
OpenAlex ID: W4407346709