Pancreatitis, Polyarthritis and Panniculitis (PPP) Syndrome - A Rare Presentation
Year: 2025
Type: article
Study design: Case Report
Abstract: Pancreatitis, panniculitis, and polyarthritis (PPP) syndrome is a rare manifestation (prevalence 2%-3%) of underlying pancreatic pathology which is characterized by fat necrosis in subcutaneous tissue and joints. The widely accepted etiological hypothesis is systemic dissemination of pancreatic lipase. It has a mortality rate approaching 25%. We present a case of pancreatitis, panniculitis, and polyarthritis syndrome in a 52-year-old man with chronic pancreatitis complicated by pancreatico-pericardial fistula.
Source: ACG Case Reports Journal
Authors: Devank Shah, Rupesh Pokharna, Sudhir Maharshi, Kamleshkumar Sharma, Prerak Maniar
Institutions: SMS Medical College, Sawai Man Singh Hospital
Language: English
Subfield: Surgery
Field: Medicine
Domain: Health Sciences
Open Access status: diamond
OpenAlex ID: W4407624578
