Work

Skeletonized Handmade Valved Conduit: A Novel Approach for Transannular Repair in Absent Pulmonary Valve Syndrome

Year: 2025

Type: article

Abstract: Absent pulmonary valve syndrome in neonates and infants presents challenges due to airway compression from dilated pulmonary arteries and limited anatomical space for right ventricular outflow tract (RVOT) reconstruction. This study introduces a half-skeletonized handmade valved conduit for transannular repair in a 6-month-old boy with absent pulmonary valve syndrome, trisomy 21, and laryngomalacia. The conduit, made from expanded polytetrafluoroethylene, provided effective RVOT reconstruction while minimizing airway obstruction. Postoperative imaging confirmed bronchial decompression, and echocardiography showed sustained valve function at 1 year. This technique addresses homograft limitations and may have broader applicability in congenital heart defects requiring RVOT reconstruction.

Source: Annals of Thoracic Surgery Short Reports

DOI: 10.1016/j.atssr.2025.01.023

Authors: Hiroki Ito, Keiichi Hirose, Kisaburo Sakamoto, Akio Ikai

Institutions: Shizuoka Children's Hospital, Shizuoka General Hospital

Language: English

Topic: Congenital Heart Disease Studies

Subfield: Epidemiology

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: gold

Estimated APC paid: $975