Work

Paediatric Para-Meningeal Alveolar Rhabdomyosarcoma in the Nasal Cavity

Year: 2025

Type: article

Abstract: ABSTRACT Introduction Rhabdomyosarcoma is the second most common malignant soft tissue tumor, which is of skeletal muscle in origin. Alveolar subtype of rhabdomyosarcoma is commonly seen in 10-25 years of age. We present a rare case of alveolar rhabdomyosarcoma in a one year old child. Case report A one-year-old boy presented with swelling and nasal discharge in the left nasal cavity of two months duration. Examination showed a smooth pink-coloured mass in the left nasal cavity arising from the lateral wall. Fine needle aspiration cytology, biopsy, imaging studies and immunohistochemistry were done and a diagnosis of alveolar rhabdomyosarcoma confirmed. Treatment was done by chemoradiation. Discussion Biopsy and immunohistochemistry are the gold standard investigations for rhabdomyosarcoma. It requires a multimodal treatment approach including surgery, chemotherapy, and radiotherapy. Keywords Rhabdomyosarcoma; Paediatric malignancy; Para meningeal; Alveolar; Nasal cavity

Source: Bengal Journal of Otolaryngology and Head Neck Surgery

DOI: 10.47210/bjohns.2024.v32i2.89

Authors: Cindya Vidyadharan, Aju Ravindran, Divya Bharathan

Institution: Malabar Medical College Hospital and Research Centre

Language: English

Topic: Sarcoma Diagnosis and Treatment

Subfield: Pulmonary and Respiratory Medicine

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: gold

Estimated APC paid: $60