Work

Cerebral Proliferative Arteriopathy Secondary to Extracranial Carotid Stenosis

Year: 2025

Type: article

Abstract: Cerebral proliferative arteriopathy (CPA) is a rare vascular malformation distinct from arteriovenous malformations. Although arterial stenoses in CPA are thought to develop later, we hypothesize some cases may result from preexisting stenosis causing ischemia and vascular proliferation. A 7-year-old boy with a history of biliary atresia and a traumatic jugular line insertion presented with recurrent left hemiparesis. Magnetic resonance imaging and cerebral angiography revealed a pinhole stenosis in the right internal carotid artery and CPA features. This case suggests CPA may be a secondary maladaptive response to chronic ischemia in certain patients.

Source: Annals of Internal Medicine Clinical Cases

DOI: 10.7326/aimcc.2024.1079

Authors: Phone Myat, Richard Shaw, Mark Dexter, Kartik Bhatia

Institutions: UNSW Sydney, Children's Hospital at Westmead, The University of Sydney

Language: English

Topic: Cerebrovascular and Carotid Artery Diseases

Subfield: Pulmonary and Respiratory Medicine

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: diamond

OpenAlex ID: W4409451397

FWCI: 0.593

Cites: 8

Cited by: 1

Related to: 10