Work

Atriofascicular pathway in Ebstein's anomaly: Revisiting the role of preoperative EP studies in pediatrics

Year: 2025

Type: article

Abstract: We present a case of a 6-year-old with Ebstein's anomaly (EA) who was found to have a right lateral decremental, antegrade only accessory pathway (AP), presumed atriofascicular AP, during a pre-operative electrophysiology study (EPS) prior to da Silva Cone repair (CR). Atriofascicular APs represent <3 % of APs but have an association with EA. To the best of our knowledge, this is the youngest reported case of EA with an atriofascicular AP. Providers should be aware of this possibility, as CRs are being done at younger ages, and they may be discovered in asymptomatic patients.

Source: Journal of Electrocardiology

DOI: 10.1016/j.jelectrocard.2025.154053

Authors: Brock A. Karolcik, Lee B. Beerman, Christopher W. Follansbee, Gaurav Arora

Institutions: UPMC Health System, Children's Hospital of Pittsburgh, University of Pittsburgh Medical Center

Language: English

Topic: Cardiac Arrhythmias and Treatments

Subfield: Cardiology and Cardiovascular Medicine

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: hybrid

Estimated APC paid: $2,890