Work

Kidney Involvement in Erdheim-Chester Disease

Year: 2025

Type: article

Abstract: Erdheim-Chester disease (ECD) is a rare histiocytosis belonging to the L group,S1 with an annual incidence of fewer than 0.5 cases/1’000’000 adults in Western Europe.1 Growing awareness and improved recognition have led to a consistently increasing number of diagnoses: over 2000 cases have been recognised to date, and over 600 patients are currently under follow-up worldwide –likely an underestimate of the true prevalence.

Source: Kidney International Reports

DOI: 10.1016/j.ekir.2025.06.020

Authors: Emanuele D’Arpino, Francesco Pegoraro, Augusto Vaglio, Francesco Peyronel

Institutions: University of Florence, Meyer Children's Hospital, Azienda Ospedaliero-Universitaria Careggi

Language: English

Topic: Histiocytic Disorders and Treatments

Subfield: Physiology

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: gold

Estimated APC paid: $2,800