Work

Unmasking Partial Shone Complex: A Late Diagnosis with Rare Associations

Year: 2025

Type: article

Abstract: Shone complex (SC), also known as Shone syndrome, is a rare congenital heart disease first described in 1963 that involves the coexistence of 4 left ventricular (LV) inflow and outflow obstructions including a parachute mitral valve (PMV), supravalvular mitral ring, subvalvular aortic stenosis (AS), and aortic coarctation. The incomplete form, or partial SC, involves only 2 or 3 of these anomalies.1 Inflow obstructions include PMV, supravalvular mitral ring (supravalvular ring of the left atrium), or congenital mitral stenosis (MS).

Source: CASE

DOI: 10.1016/j.case.2025.05.007

Authors: Mariam Zunnu Rain, Mishita Goel, Mariam Raheem, Ahmad El-Moussa, Randy Lieberman, Luis Afonso

Institutions: Wayne State University, Detroit Medical Center

Language: English

Topic: Congenital Heart Disease Studies

Subfield: Epidemiology

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: gold

Estimated APC paid: $950