Work

Undiagnosed interrupted aortic arch presenting with acute aortic dissection in a teenager: A rare case and successful repair

Year: 2025

Type: article

Abstract: Acute aortic dissection in the pediatric population is an extremely rare but life-threatening condition. The estimated incidence is less than 0.5 per million children annually.1 Most reported cases are associated with genetic aortopathies, including Marfan syndrome, Loeys-Dietz syndrome, and Ehlers-Danlos syndrome, although even in these cohorts, dissection during childhood or adolescence is uncommon. Interrupted aortic arch (IAA) is a rare congenital cardiac anomaly that represents approximately 1% of all congenital heart defects, with an incidence of about 3 per 1,000,000 live births.

Source: JTCVS structural and endovascular.

DOI: 10.1016/j.xjse.2025.100085

Authors: İlke Keleş Selek, Çağla Canbay Sarılar, Birol Akdoğan, Sinan Bulut, Celal Caner Ercan, Sertaç Çiçek

Institution: Istanbul University

Language: English

Topic: Aortic Disease and Treatment Approaches

Subfield: Pulmonary and Respiratory Medicine

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: gold

Estimated APC paid: $2,500