Work

A Unique Case of Pure Bilateral Lambdoid Craniosynostosis and Progression to Mercedes-Benz Syndrome Following Spring Cranioplasty

Year: 2025

Type: article

Abstract: We report a case of a 3-month-old female with isolated bilateral lambdoid craniosynostosis treated by suturectomy with cranial springs, who later demonstrated unexpected sagittal fusion. The patient presented with bilateral lambdoid and mendosal fusion producing a distinctive posterior vault deformity. Springs placed at suturectomy were removed five months later. Segmented CT analysis revealed intracranial volume expansion from 727.4 cm 3 pre-op to 1371.9 cm 3 post-removal, with minimal blood loss and uncomplicated recovery. Post-removal imaging showed complete sagittal synostosis, suggesting either a delayed manifestation of Mercedes-Benz pattern synostosis or a mechanically induced secondary synostosis due to springs, warranting further investigation.

Source: The Cleft Palate-Craniofacial Journal

DOI: 10.1177/10556656251389537

Authors: Sebastian Kuriakose, Yasmine Soubra, Sarah Anne Frommer, Elizabeth Tyler-Kabara, Patrick K Kelley

Institutions: The University of Texas at Austin, Texas A&M University, Dell Children's Medical Center of Central Texas

Language: English

Topic: Craniofacial Disorders and Treatments

Subfield: Genetics

Field: Biochemistry, Genetics and Molecular Biology

Domain: Life Sciences

SDG: Good health and well-being

Open Access status: hybrid

Estimated APC paid: $4,150