Late Onset Congenital Cystic Adenomatoid Pulmonary Malformation
Year: 2025
Type: article
Study design: Case Report
Abstract: Congenital cystic adenomatoid pulmonary malformations are defined as the presence of a cystic mass of undifferentiated lung tissue; a third of the cases affect one of the lower lobes, and multilobar or bilateral affection is rare. The entity is a rare congenital malformation in the lungs, with an incidence of one in 11,000 to one in 35,000 live births. It is mainly discovered during the fetal period, although a low percentage of patients will be diagnosed postnatally. The disease has a wide spectrum of clinical manifestations, from asymptomatic to life-threatening respiratory symptoms. The diagnosis is made by imaging studies, and the treatment depends on the patient's clinical status. We reported the case of an infant with a rare congenital pulmonary airway malformation and a late diagnosis, which makes the case even rarer, who required open lobectomy as treatment. Keywords: Congenital abnormalities; cystic adenomatoid malformation of lung; lung diseases.
Language: English
Subfield: Surgery
Field: Medicine
Domain: Health Sciences
Open Access status: diamond
OpenAlex ID: W4415837156
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