Year: 2025
Type: article
Study design: Case Report
Abstract: Pheochromocytoma is often not the first diagnosis considered for many neurological complaints, especially obstructive hydrocephalus. We report a case of Von Hippel-Lindau disease in an adolescent presenting with obstructive hydrocephalus due to adrenergic storm requiring emergency ventriculoperitoneal shunt. This vignette emphasizes the importance of an integral approach, particularly accurate diagnosis that would lead to targeted pharmacological therapy focusing on alphaa-drenergic receptor blockade, which was followed by total curative excision of pheochromocytoma in a timely fashion.
Authors: Cheah Jean Mun, Thai Lun Tan, Stefanie Hung, Fei Bing Yong, Sue Wen Lim, Xin-Yi Ooi, Hui Chin Wong, Sy Liang Yong
Institutions: Ministry of Health, Tengku Ampuan Rahimah Hospital
Language: English
Subfield: Surgery
Field: Medicine
Domain: Health Sciences
Open Access status: diamond
OpenAlex ID: W4416606974