Congenital Left Atrial Mitral Accessory Chord With Accessory Mitral Valve Tissue Causing Dual-Valve Regurgitation
Year: 2025
Type: article
Study design: Case Report
Abstract: BACKGROUND: Left atrial mitral valve (MV) accessory chord and accessory MV tissue are rare congenital anomalies that may mimic more common pathologies. CASE SUMMARY: A 30-year-old man presented with dyspnea, weight loss, and an outpatient transthoracic echocardiogram concerning for infective endocarditis. Transesophageal echocardiography revealed a chordlike structure extending from the limbus of the interatrial septum to the anterior MV leaflet, continuing through the left ventricular outflow tract, across the aortic valve, and into the ascending aorta. These findings were associated with moderate mitral regurgitation and severe aortic regurgitation. Surgical resection confirmed the diagnosis of accessory MV tissue with a left atrial MV accessory chord. DISCUSSION: Patients may present with heart failure or malperfusion symptoms due to valvopathy or left ventricular outflow tract obstruction. Multimodal imaging and surgical resection with valve repair are key to diagnosis and management. TAKE-HOME MESSAGES: Chordal anomalies can mimic endocarditis and cause dual-valve disease. Early transesophageal echocardiography and surgical intervention are critical to avoid misdiagnosis.
Source: JACC Case Reports
Authors: Muhammad Salman Sabri, Fahad Waqar, Eddy Mizrahi, Andrew Fireman, Robert Watson, James L. West, Mauricio Garrido
Language: English
Subfield: Cardiology and Cardiovascular Medicine
Field: Medicine
Domain: Health Sciences
Open Access status: gold
Estimated APC paid: $850
OpenAlex ID: W4416912181