Adult‐Onset Still's Disease Complicated by Secondary Hemophagocytic Lymphohistiocytosis: A Case Report
Year: 2025
Type: article
Study design: Case Report
Abstract: Adult-onset Still's disease (AOSD) is a rare autoinflammatory disorder characterized by fever, rash, joint pain, and elevated ferritin levels. Systemic inflammation can trigger an exaggerated immune response, leading to secondary hemophagocytic lymphohistiocytosis (HLH). This case discusses AOSD complicated by HLH in a 29-year-old female, emphasizing prompt recognition and management.
Source: Clinical Case Reports
DOI: 10.1002/ccr3.71650
Language: English
Subfield: Hematology
Field: Medicine
Domain: Health Sciences
Open Access status: gold
Estimated APC paid: $1,820
OpenAlex ID: W4417311411
