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Surgical Strategies of Staged Spinal Traction–Fusion for Severe Scoliosis in Osteogenesis Imperfecta Type IV: A Case Report and Literature Review

Year: 2025
Type: article
Study design: Case Report
Abstract: BACKGROUND: To describe a staged surgical protocol combining halo-pelvic traction (HPT) and posterior spinal fusion (PSF) for severe scoliosis in a patient with osteogenesis imperfecta (OI) type IV and to evaluate its outcomes. Given the paucity of population-level data on spinal orthoses in OI, this report highlights a tailored surgical approach for this high-risk population. CASE PRESENTATION AND MANAGEMENT: A 16-year-old girl with OI type IV and progressive scoliosis underwent a 2-stage correction: (1) preoperative HPT for 3 months to reduce coronal deformity and optimize spinal alignment, followed by (2) PSF with all-pedicle-screw instrumentation. The staged protocol achieved successful deformity correction without neurological or implant-related complications. All pedicle screws were safely placed despite osteopenic bone. At follow-up, radiographic outcomes were maintained, and the patient reported improved posture and function. Minor surgical differences and literature review are highlighted for multimodal management. CONCLUSION: Progressive scoliosis in patients with OI can be effectively managed through structured, phased therapeutic programs, with the combined approach of HPT and PSF representing a significant surgical intervention strategy. CLINICAL RELEVANCE: The clinical significance of this approach lies in transforming the management of a challenging rare disease-progressive scoliosis in osteogenesis imperfecta-from an empirical endeavor into a structured, systematic clinical pathway, while providing a validated technical combination for its most critical surgical intervention.
Language: English
Subfield: Surgery
Field: Medicine
Open Access status: diamond
OpenAlex ID: W7117466703
FWCI: 0.892
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Cited by: 1
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