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Silent Battle within the Bag of Worms – A Rare Case Report of Plexiform Neurofibroma

Year: 2025

Type: article

Abstract: Plexiform neurofibroma (PNF) is a tumor of the peripheral nerve sheath involving multiple nerve fascicles as deforming masses within connective tissue and skin. It manifests early in life and is associated with neurofibromatosis type 1 and may transform into a malignant peripheral nerve sheath tumor. A pathognomonic sign of this condition is the “Bag of Worms,” which is also observed in this case along with other characteristic features. Along with the facial features, changes are also observed in the maxilla and mandible. We report a rare case of a 14-year-old female with diagnosed PNF involving oral features.

Source: Journal of Indian Academy of Oral Medicine and Radiology

DOI: 10.4103/jiaomr.jiaomr_73_25

Authors: S Nivetha, C Tinky Bose, Keerthy K Mukundan, Susha Grace Thomas

Institution: Kerala University of Health Sciences

Language: English

Topic: Neurofibromatosis and Schwannoma Cases

Subfield: Neurology

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: diamond

OpenAlex ID: W7117512216

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Cites: 8

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