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Severe hypoxaemia and intrapulmonary vascular dilatations associated with long-term luspatercept therapy

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Year: 2026
Type: article
Study design: Case Report
Source: European Respiratory Journal
DOI: 10.1183/13993003.01603-2025
Authors: Marina Gueçamburu, Pierre Schilfarth, Xavier Demant, Sophie Dimicoli-Salazar, Aurélien Lamor-Fauthoux, Marc Humbert, David Montani, Christophe Guignabert, Laurent Savale, Arnaud Maurac
Institutions: Centre Hospitalier Universitaire de Bordeaux, Hôpital Cardiologique du Haut-Lévêque, Inserm, Université Paris-Saclay, Assistance Publique – Hôpitaux de Paris, Hypertension pulmonaire : physiopathologie et innovation thérapeutique, Bicêtre Hospital, Centre de Recherche Cardio-Thoracique de Bordeaux
Language: English

Topic: Pulmonary Hypertension Research and Treatments
Subfield: Pulmonary and Respiratory Medicine
Field: Medicine
Domain: Health Sciences
SDG: Good health and well-being

Open Access status: closed
OpenAlex ID: W7124241078
FWCI: 4.463
Cites: 9
Cited by: 1
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