Scimitar Syndrome Incidentally Identified During the Workup for Acute Appendicitis in a Young Adult Female: A Case Report
Year: 2026
Type: article
Study design: Case Report
Abstract: While congenital pulmonary venolobar syndrome (CPVS), including Scimitar syndrome and horseshoe lung, is highly uncommon in adults, acute appendicitis is a common surgical emergency. This case report emphasizes the difficulties in diagnosing patients and the possibility of misdiagnosis, highlighting the significance of clinical awareness for the best possible care. A laparoscopic appendectomy was performed on a 21-year-old female patient who presented with symptoms of acute appendicitis. During the procedure, a suspicious cecal tumor and a subserosal, dilated retrocecal appendix were observed. The patient was identified as having right lung hypoplasia, cardiac dextroposition, and partial anomalous pulmonary venous return (PAPVR), indicating the presence of Scimitar syndrome along with horseshoe lung. These findings were confirmed by post-operative CT imaging. The appendix histopathology and colonoscopy were unremarkable, and the cardiac assessment, including the electrocardiogram and echocardiogram, was also normal. Incidental CPVS in adults requires diligent recognition for optimal management. This case contributes to the limited research on adult manifestations of Scimitar syndrome and associated abnormalities, which is expanded by this instance.
Source: Cureus
Language: English
Subfield: Epidemiology
Field: Medicine
Domain: Health Sciences
Open Access status: diamond
OpenAlex ID: W7125242335