Work

Rare Case of Multifocal Spinal Hemangioblastomas With Holocord Syringo-Hydromyelia in an Adolescent Male

Year: 2026

Type: article

Abstract: Hemangioblastomas are benign, highly vascular tumors of the central nervous system. Although they most commonly arise in the cerebellum, they may also involve the brainstem and spinal cord. The presence of multiple spinal hemangioblastomas is frequently associated with von Hippel-Lindau (VHL) syndrome; however, sporadic cases without an underlying genetic syndrome can occur. Characteristic imaging features include avid post-contrast enhancement, associated syrinx formation, and intratumoral or peritumoral flow voids. Spinal hemangioblastomas account for a small proportion of intramedullary spinal tumors and are rarely reported in adolescents. We present a rare case of multifocal spinal hemangioblastomas with extensive holocord syringo-hydromyelia in an adolescent male patient without any evidence of VHL syndrome.

Source: Cureus

DOI: 10.7759/cureus.102651

Authors: Rishi Meswani, Prashant Onkar, Suresh Phatak, Kajal Mitra, Mayank Rangari

Institutions: NKP Salve Institute of Medical Sciences and Lata Mangeshkar Hospital, Datta Meghe Institute of Higher Education and Research, Manipal Hospital

Language: English

Topic: Ear and Head Tumors

Subfield: Oncology

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: diamond

OpenAlex ID: W7126245443