Work

Neuroradiologic appearance of intracranial vascular lesions associated with multiple lymphangioendotheliomatosis with thrombocytopenia

Year: 2026

Type: article

Abstract: Multifocal lymphangioendotheliomatosis with thrombocytopenia (MLT) is a rare congenital vascular disorder characterized by a multitude of lesions involving the skin and gastrointestinal tract with associated thrombocytopenia. Due to the rarity of this disorder, the incidence of intracranial involvement is unknown and only 6 cases have been described in the literature to date. Here we present a case of MLT with a series of neuroimaging studies across several years of the patient's life showcasing the natural history of the intracranial vascular lesions associated with MLT. The features presented in this case report highlight the importance of CNS imaging in patients with MLT in both emergent and nonemergent settings.

Source: Radiology Case Reports

DOI: 10.1016/j.radcr.2026.01.050

Authors: Lamson D. Tran, Oswaldo A. Guevara Tirado, Vivienne Pham, Afshan Z. Ara, Stephen F. Kralik

Institutions: Texas A&M University, Ponce Health Sciences University, Baylor College of Medicine, Case Western Reserve University, Texas Children's Hospital

Language: English

Topic: Vascular Malformations and Hemangiomas

Subfield: Surgery

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: gold

Estimated APC paid: $600