Work

Unmasking the Stenosis: Simultaneous Mitral Valve Replacement and Scimitar Vein Rerouting in a Dextro-Rotated Heart

Year: 2026

Type: article

Abstract: Scimitar syndrome (SS) is a rare congenital condition marked by partial anomalous pulmonary venous connection, dextroposition of the heart, right lung hypoplasia, and systemic arterial supply to the right lung. Also known as congenital veno-lobar syndrome and other names, it has been classified into three types by Lupius et al. A significant number of cases are associated with congenital heart anomalies, while association with acquired cardiac disease is rare. We present the rare case of a 39-year-old woman with exertional dyspnoea during pregnancy, initially diagnosed with mild mitral stenosis, later found to have SS with rheumatic heart disease.

Source: Cureus

DOI: 10.7759/cureus.106248

Authors: Vimlendra K Chaudhary, Deepak G, Sowmya Ramanan, Baiju Sasi Dharan

Institution: Sree Chitra Thirunal Institute for Medical Sciences and Technology

Language: English

Topic: Congenital Heart Disease Studies

Subfield: Epidemiology

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: diamond

OpenAlex ID: W7147066691