Work

When Ebstein Meets Fallot

Year: 2026

Type: article

Abstract: CASE SUMMARY: A 14-year-old boy was admitted after resuscitated ventricular fibrillation. He had tetralogy of Fallot associated with Ebstein's anomaly, surgically repaired at age 7 without tricuspid intervention. His ECG demonstrates overlapping features of both conditions: high-amplitude right bundle branch block and right ventricular hypertrophy consistent with repaired tetralogy of Fallot, along with broad "Himalayan" P waves, first-degree atrioventricular block, and fragmented QRS complexes reflecting Ebstein-related conduction abnormalities. This electrocardiographic coexistence illustrates how dual congenital substrates may converge into a single electrical phenotype. TAKE-HOME MESSAGES: An atypical ECG pattern in congenital heart disease may unmask an associated anomaly. Fragmented QRS in Ebstein's anomaly is a potential marker of increased arrhythmic risk.

Source: JACC Case Reports

DOI: 10.1016/j.jaccas.2026.107400

Authors: Jules Ader, Charlène Bredy, Jean-Luc Pasquié

Institutions: Centre Hospitalier Universitaire de Montpellier, Hôpital Arnaud de Villeneuve

Language: English

Topic: Congenital Heart Disease Studies

Subfield: Epidemiology

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: gold

Estimated APC paid: $850