Surgical resection of a solid posterior cranial fossa hemangioblastoma causing obstructive hydrocephalus in a pediatric patient
Year: 2026
Type: article
Study design: Case Report
Abstract: Background: Hemangioblastomas (HBs) are vascular neoplasms that are most involved with the central nervous system and can be associated with Von Hippel-Lindau disease (VHL). HBs involving pediatric patients are common, but VHL-associated HBs and those that cause obstructive hydrocephalus are rare. Case Description: In this case study, a pediatric patient presented with multiple neurological deficits including headaches, ataxia, confusion, and right-sided weakness, as well as a magnetic resonance image revealing a lesion involving the 4 th ventricle causing obstructive hydrocephalus. An external ventricular drain was placed to treat the hydrocephalus acutely, followed by a tumor resection, resulting in some postsurgical bleeding and increased fluid accumulation. Further genetic testing revealed that the patient was positive for a VHL mutation. Conclusion: There are only a few reports of intraventricular HBs that are found in the 4 th ventricle in pediatric patients with less discussing solid HBs, so evaluation of this case can provide a valuable opportunity to compare and reflect on the nature of this rare presentation and contribute toward understanding the best approaches for treating these rare conditions.
Source: Surgical Neurology International
DOI: 10.25259/sni_45_2026
Language: English
Topic: Ear and Head Tumors
Subfield: Oncology
Field: Medicine
Domain: Health Sciences
Open Access status: green
OpenAlex ID: W7162103889