Work

Congenital Atrophic Dermatofibrosarcoma Protuberans: A Case Report and Narrative Review of the Literature

Year: 2026

Type: review

Abstract: Dermatofibrosarcoma protuberans is a rare dermal and subcutaneous soft-tissue tumor, uncommon in children, characterized by CD34 positivity and COL1A1-PDGFB fusion. Prognosis is generally good, but local recurrence risk is high, so complete excision with clear margins and six-monthly follow-up for three years after surgery is recommended in most cases.

Source: Clinical Case Reports

DOI: 10.1002/ccr3.73010

Authors: Sima Shamshiri Khamene, Izat Mohammad Khawajah, Taha Shahbazi, Safoura Shakoei

Institutions: Razi Hospital, Razi Hospital, Tehran University of Medical Sciences, Imam Khomeini Hospital

Language: English

Topic: Soft tissue tumor case studies

Subfield: Rheumatology

Field: Medicine

Domain: Health Sciences

SDG: Good health and well-being

Open Access status: gold

Estimated APC paid: $1,820