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Persistence of static lung hyperinflation in adults with cystic fibrosis treated with elexacaftor-tezacaftor-ivacaftor

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Year: 2026
Type: article
Study design: Observational Study
Source: Thorax
DOI: 10.1136/thorax-2026-225174
Authors: Théo Dhote, Clémence Martin, Isabelle Fajac, Frédérique Aubourg, Reem Kanaan, Nicolas Carlier, Isabelle Honoré, Johanna Fesenbeckh, Jennifer Da Silva, Thierry Perez, Pierre-Régis Burgel
Institutions: Centre National de la Recherche Scientifique, Inserm, Université Paris Cité, Hôpital Cochin, Assistance Publique – Hôpitaux de Paris, Institut Cochin, ERN LUNG, Centre Hospitalier Universitaire de Lille, Center for Infection and Immunity of Lille
Language: English

Topic: Cystic Fibrosis Research Advances
Subfield: Pulmonary and Respiratory Medicine
Field: Medicine
Domain: Health Sciences
SDG: Good health and well-being

Open Access status: closed

Funder: Association Vaincre la Mucoviscidose
OpenAlex ID: W7203684798
FWCI:
Cites: 34
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