Year: 2026
Type: article
Study design: Case Report
Abstract: We report a case of IgG4-related disease in a 65-year-old man who remained undiagnosed for two decades. His disease initially manifested as periorbital oedema, followed by right cheek swelling, lymphadenopathy and a widespread pruritic eruption of skin-coloured and pale erythematous papules. IgG4 was only considered after a stroke protocol MRI of the brain demonstrated an incidental finding of characteristic orbital manifestations. This case highlights the diagnostic complexity of IgG4-related disease and emphasises the importance of recognising its varied presentations to facilitate early diagnosis and management.
DOI: 10.1111/ajd.70229
Institutions: Westmead Hospital, The University of Sydney, NSW Health Pathology
Language: English
Subfield: Rheumatology
Field: Medicine
Domain: Health Sciences
Open Access status: bronze
OpenAlex ID: W7225448407