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Yuichi Matsushima

Mitochondrial Lon protease regulates mitochondrial DNA copy number and transcription by selective degradation of mitochondrial transcription factor A (TFAM)
2010 · Yuichi Matsushima, Yu-ichi Goto, et al. · Proceedings of the National Academy of Sciences · 294
Mitochondrial Complex III Deficiency Caused by a HomozygousUQCRC2Mutation Presenting with Neonatal-Onset Recurrent Metabolic Decompensation
2012 · Noriko Miyake, Shoji Yano, et al. · Human Mutation · 88
A homozygous mutation of C12orf65 causes spastic paraplegia with optic atrophy and neuropathy (SPG55)
2012 · Haruo Shimazaki, Yoshihisa Takiyama, et al. · Journal of Medical Genetics · 87
Drosophila Mitochondrial Transcription Factor B2 Regulates Mitochondrial DNA Copy Number and Transcription in Schneider Cells
2004 · Yuichi Matsushima, Rafael Garesse, et al. · Journal of Biological Chemistry · 85
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Drosophila Mitochondrial Transcription Factor B1 Modulates Mitochondrial Translation but Not Transcription or DNA Copy Number in Schneider Cells
2005 · Yuichi Matsushima, Cristina Adán, et al. · Journal of Biological Chemistry · 76
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ECHS1 Mutations Cause Combined Respiratory Chain Deficiency Resulting in Leigh Syndrome
2014 · Chika Sakai, Seiji Yamaguchi, et al. · Human Mutation · 68
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Functional Domains of Chicken Mitochondrial Transcription Factor A for the Maintenance of Mitochondrial DNA Copy Number in Lymphoma Cell Line DT40
2003 · Yuichi Matsushima, Kiyoshi Matsumura, et al. · Journal of Biological Chemistry · 61
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Matrix proteases in mitochondrial DNA function
2011 · Yuichi Matsushima, Laurie S. Kaguni · Biochimica et Biophysica Acta (BBA) - Gene Regulatory Mechanisms · 59
Cardiomyocyte-specific loss of mitochondrial p32/C1qbp causes cardiomyopathy and activates stress responses
2017 · Toshiro Saito, Takeshi Uchiumi, et al. · Cardiovascular Research · 58
Doxycycline induces apoptosis via ER stress selectively to cells with a cancer stem cell-like properties: importance of stem cell plasticity
2017 · Takashi Matsumoto, Takeshi Uchiumi, et al. · Oncogenesis · 54
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Physiological and Biochemical Defects in Functional Interactions of Mitochondrial DNA Polymerase and DNA-binding Mutants of Single-stranded DNA-binding Protein
2004 · Carol L. Farr, Yuichi Matsushima, et al. · Journal of Biological Chemistry · 53
The Tor and Sin3-Rpd3 complex regulate expression of the mitophagy receptor protein Atg32
2014 · Masamune Aihara, Xiulian Jin, et al. · Journal of Cell Science · 47
Drosophila mitochondrial transcription factor A (d-TFAM) is dispensable for the transcription of mitochondrial DNA in Kc167 cells
2001 · Akira GOTO, Yuichi MATSUSHIMA, et al. · Biochemical Journal · 46
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Differential Phenotypes of Active Site and Human Autosomal Dominant Progressive External Ophthalmoplegia Mutations in Drosophila Mitochondrial DNA Helicase Expressed in Schneider Cells
2007 · Yuichi Matsushima, Laurie S. Kaguni · Journal of Biological Chemistry · 43
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Neural-specific deletion of mitochondrial p32/C1qbp leads to leukoencephalopathy due to undifferentiated oligodendrocyte and axon degeneration
2017 · Mikako Yagi, Takeshi Uchiumi, et al. · Scientific Reports · 41
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IBA57 mutations abrogate iron-sulfur cluster assembly leading to cavitating leukoencephalopathy
2017 · Akihiko Ishiyama, Chika Sakai, et al. · Neurology Genetics · 39
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A Large DNA-binding Nuclear Protein with RNA Recognition Motif and Serine/Arginine-rich Domain
1996 · Hidetoshi Inagaki, Yuichi Matsushima, et al. · Journal of Biological Chemistry · 38
Mitochondrial Transcription Factor B2 Is Essential for Metabolic Function in Drosophila melanogaster Development
2008 · Cristina Adán, Yuichi Matsushima, et al. · Journal of Biological Chemistry · 37
Mitochondrial Lon protease is a gatekeeper for proteins newly imported into the matrix
2021 · Yuichi Matsushima, Kazuya Takahashi, et al. · Communications Biology · 36
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Drosophila protease ClpXP specifically degrades DmLRPPRC1 controlling mitochondrial mRNA and translation
2017 · Yuichi Matsushima, Yuta Hirofuji, et al. · Scientific Reports · 28
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Coiled Coil Domain-containing Protein 56 (CCDC56) Is a Novel Mitochondrial Protein Essential for Cytochrome c Oxidase Function
2012 · Susana Peralta, Paula Clemente, et al. · Journal of Biological Chemistry · 26
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Isolation of Rat Mitochondrial Transcription Factor A (r-Tfam) cDNA
2000 · Hidetoshi Inagaki, Toshihiko Hayashi, et al. · DNA sequence · 25
Modeling Pathogenic Mutations of Human Twinkle in Drosophila Suggests an Apoptosis Role in Response to Mitochondrial Defects
2012 · Alvaro Sanchez-Martinez, Manuel Calleja, et al. · PLoS ONE · 24
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Physiological and Biochemical Defects in Carboxyl-terminal Mutants of Mitochondrial DNA Helicase
2008 · Yuichi Matsushima, Carol L. Farr, et al. · Journal of Biological Chemistry · 24
Interferons Suppress Mitochondrial Gene Transcription by Depleting Mitochondrial Transcription Factor A (mtTFA)
1997 · HIDETOSHI INAGAKI, YUICHI MATSUSHIMA, et al. · Journal of Interferon & Cytokine Research · 21
Works count: 53
Citation count: 1,634
H-index: 24
I10-index: 36
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