Author

Cameron A. Ackerley

Observed names: C. A. Ackerley, CAMERON ACKERLEY, Cameron A Ackerley, Cameron ACKERLEY, Cameron Ackerley

Institutions: University of Toronto, Hospital for Sick Children

Observed institutions: BC Cancer Agency, Centre National de la Recherche Scientifique, St. Michael's Hospital, Sunnybrook Health Science Centre, Scuola Superiore Sant'Anna, University of Toronto, Great Ormond Street Hospital, Middlemore Hospital, Hospital for Sick Children, Toronto General Hospital, Fred Hutch Cancer Center, Istituto di Fisiologia Clinica, Institut de génétique et de développement de Rennes, Ontario Veterinary College, Université de Montréal, University of Guelph, The University of Texas Southwestern Medical Center

OpenAlex ID: A5113523190

Expression of the cystic fibrosis gene in non-epithelial invertebrate cells produces a regulated anion conductance

1991 · Norbert Kartner, John W. Hanrahan, et al. · Cell · 495

L-type Ca2+ channels provide a major pathway for iron entry into cardiomyocytes in iron-overload cardiomyopathy

2003 · Gavin Y Oudit, Hui Sun, et al. · Nature Medicine · 474

Targeted inactivation of sister of P-glycoprotein gene ( spgp ) in mice results in nonprogressive but persistent intrahepatic cholestasis

2001 · Renxue Wang, Myriam Salem, et al. · Proceedings of the National Academy of Sciences · 333

Mutations in NHLRC1 cause progressive myoclonus epilepsy

2003 · Elayne M Chan, Edwin J Young, et al. · Nature Genetics · 325

Presenilin-1, Nicastrin, Amyloid Precursor Protein, and γ-Secretase Activity Are Co-localized in the Lysosomal Membrane

2003 · Stephen H. Pasternak, Richard D. Bagshaw, et al. · Journal of Biological Chemistry · 314

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Atelectasis Causes Vascular Leak and Lethal Right Ventricular Failure in Uninjured Rat Lungs

2003 · Michelle Duggan, Conán L. McCaul, et al. · American Journal of Respiratory and Critical Care Medicine · 184

The role of the LRPPRC (leucine-rich pentatricopeptide repeat cassette) gene in cytochrome oxidase assembly: mutation causes lowered levels of COX (cytochrome c oxidase) I and COX III mRNA

2004 · Fenghao XU, Charles MORIN, et al. · Biochemical Journal · 174

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Expanded Repeat in Canine Epilepsy

2005 · Hannes Lohi, Edwin J. Young, et al. · Science · 170

Characteristic Multiorgan Pathology of Cystic Fibrosis in a Long-Living Cystic Fibrosis Transmembrane Regulator Knockout Murine Model

2004 · Peter R. Durie, Geraldine Kent, et al. · American Journal Of Pathology · 160

Lafora disease

2016 · Julie Turnbull, Erica Tiberia, et al. · Epileptic Disorders · 156

Novel glycogen synthase kinase 3 and ubiquitination pathways in progressive myoclonus epilepsy

2005 · Hannes Lohi, Leonarda Ianzano, et al. · Human Molecular Genetics · 152

Mutation I810N in the α3 isoform of Na + ,K + -ATPase causes impairments in the sodium pump and hyperexcitability in the CNS

2009 · Steven J. Clapcote, Steven Duffy, et al. · Proceedings of the National Academy of Sciences · 149

Defective Lung Vascular Development and Fatal Respiratory Distress in Endothelial NO Synthase-Deficient Mice

2004 · Robin N.N. Han, Saeid Babaei, et al. · Circulation Research · 144

Enhancing glioblastoma treatment using cisplatin-gold-nanoparticle conjugates and targeted delivery with magnetic resonance-guided focused ultrasound

2018 · Daniel Coluccia, Carlyn A. Figueiredo, et al. · Nanomedicine Nanotechnology Biology and Medicine · 141

PTG Depletion Removes Lafora Bodies and Rescues the Fatal Epilepsy of Lafora Disease

2011 · Julie Turnbull, Anna A. DePaoli-Roach, et al. · PLoS Genetics · 139

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VMA21 deficiency prevents vacuolar ATPase assembly and causes autophagic vacuolar myopathy

2013 · Nivetha Ramachandran, Iulia Munteanu, et al. · Acta Neuropathologica · 138

Septins Regulate Developmental Switching from Microdomain to Nanodomain Coupling of Ca2+ Influx to Neurotransmitter Release at a Central Synapse

2010 · Yi-Mei Yang, Michael J. Fedchyshyn, et al. · Neuron · 134

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Endogenous Zn2+ is required for the induction of long-term potentiation at rat hippocampal mossy fiber-CA3 synapses

2000 · You-Ming Lu, Franco A. Taverna, et al. · Synapse · 132

Peptidylarginine deiminase 2 (PAD2) overexpression in transgenic mice leads to myelin loss in the central nervous system

2008 · A. A. Musse, Z. Li, et al. · Disease Models & Mechanisms · 128

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Myelin localization of peptidylarginine deiminases 2 and 4: comparison of PAD2 and PAD4 activities

2008 · Dorothy D Wood, Cameron A Ackerley, et al. · Laboratory Investigation · 127

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Role of Multiple Drug Resistance Protein 1 in Neutral but Not Acidic Glycosphingolipid Biosynthesis

2004 · María Fabiana De Rosa, Daniel Sillence, et al. · Journal of Biological Chemistry · 113

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Glycogen hyperphosphorylation underlies lafora body formation

2010 · Julie Turnbull, Peixiang Wang, et al. · Annals of Neurology · 112

Cystic fibrosis transmembrane conductance regulator in human muscle: Dysfunction causes abnormal metabolic recovery in exercise

2010 · Anne‐Marie Lamhonwah, Christine E. Bear, et al. · Annals of Neurology · 111

The Chloride Channel ClC-4 Contributes to Endosomal Acidification and Trafficking

2003 · Raha Mohammad-Panah, Rene Harrison, et al. · Journal of Biological Chemistry · 111

Stone Formation After Augmentation Cystoplasty: The Role of Intestinal Mucus

1997 · Antoine E. Khoury, Michael Salomon, et al. · The Journal of Urology · 110

Works count: 140

Citation count: 8,668

H-index: 54

I10-index: 113