Pyloromyotomy in a Patient with Paramyotonia Congenita
Year: 2004
Type: article
Study design: Case Report
Abstract: UNLABELLED: A 2-mo-old infant with paramyotonia congenita was scheduled for pyloromyotomy and repair of inguinal hernia. Diagnosis of paramyotonia congenita was done with positive family history, myotonia at eyelids, provocation by cold, and electromyogram analysis. Anesthesia was induced via face mask with sevoflurane at 4 minimum alveolar anesthetic concentration in oxygen. Tracheal intubation was attempted without a neuromuscular relaxant. Anesthesia was maintained with sevoflurane at 0.5 minimum alveolar anesthetic concentration in oxygen and remifentanil infusion at a rate of 0.2 micro g. kg(-1). min(-1). After discontinuation of sevoflurane and remifentanil, the patient was awake and had full recovery of muscle activity. IMPLICATIONS: The literature concerning general anesthesia in paramyotonic patients is limited. We report a case of paramyotonia congenita in a 2-mo-old male infant undergoing surgery for pyloric stenosis and inguinal hernia after an uneventful anesthesia.
Source: Anesthesia & Analgesia
Authors: Binnaz Ay, Arzu Ger??ek, Varlk ??. Do??an, G??rsu Kyan, Ylmaz F. G????????
Institution: Marmara University
Language: English
Subfield: Anesthesiology and Pain Medicine
Field: Medicine
Domain: Health Sciences
Open Access status: green
OpenAlex ID: W1982911709